TIMM8A Polyclonal Antibody (E-AB-52670) elabscience
$399.00
In stock
SKU
E-AB-52670
| Size | Price (USD) |
| 200μL | $399.00 |
| 120μL | $240.00 |
| 60μL | $143.00 |
| 20μL | $73.00 |
Product Details
| Abbre | TIMM8A |
| Synonyms | DDP, DDP 1, DDP1, DFN 1, DFN1, Deafness dystonia protein 1, Deafness/dystonia peptide, MGC12262, MTS, Mitochondrial import inner membrane translocase subunit Tim8 A, TIM 8A, TIM8, TIM8A, TIMM 8A, Translocase of inner mitochondrial membrane 8 homolog A, X li, timm8a |
| Swissprot | O60220 |
| Reactivity | Human, Mouse, Rat |
| Host | Rabbit |
| Clonality | Polyclonal |
| Isotype | IgG |
| Applications | IHC |
| Conjugation | Unconjugated |
| Concentration | 1.62 mg/mL |
| Buffer | Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol. |
| Purification Method | Antigen affinity purification |
| Immunogen | Fusion protein of human TIMM8A |
| Research Areas | Neuroscience, Signal transduction |
| Cellular Localization | Mitochondrion inner membrane. |
Product Description
Background: This translocase is involved in the import and insertion of hydrophobic membrane proteins from the cytoplasm into the mitochondrial inner membrane. The gene is mutated in Mohr-Tranebjaerg syndrome/Deafness Dystonia Syndrome (MTS/DDS) and it is postulated that MTS/DDS is a mitochondrial disease caused by a defective mitochondrial protein import system. Defects in this gene also cause Jensen syndrome; an X-linked disease with opticoacoustic nerve atrophy and muscle weakness. This protein, along with TIMM13, forms a 70 kDa heterohexamer. Alternative splicing results in multiple transcript variants encoding distinct isoforms.
Storage and Shipping
| Storage | Store at -20°C Valid for 12 months. Avoid freeze / thaw cycles. |
| Shipping | The product is shipped with ice pack,upon receipt,store it immediately at the temperature recommended. |
Additional Information
| Verified Samples | Verified Samples in IHC: Human cervical cancer |
| Dilution | IHC 1:50-1:300 |
Reviews
Write Your Own Review
Related Products
Check items to add to the cart or
![Purified Anti-Mouse/Human GAL3 Antibody[M3/38] (AN003440P) elabscience](https://www.biogege.com/media/catalog/product/cache/af3f9de669682211425a7c3e7baf6e62/0/q/AN003440P_1_5394114bb5.jpg)
![FITC Anti-Human CD15/SSEA-1 Antibody[HI98] (E-AB-F1079C) elabscience](https://www.biogege.com/media/catalog/product/cache/af3f9de669682211425a7c3e7baf6e62/0/q/E-AB-F1079C_1_33c2bec8cd.jpg)
![Elab Fluor ® Violet 450 Anti-Mouse CD45R/B220 Antibody[RA3.3A 1/6.1] (E-AB-F1112UQ) elabscience](https://www.biogege.com/media/catalog/product/cache/af3f9de669682211425a7c3e7baf6e62/0/q/E-AB-F1112UQ_1_43e47286de.png)